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Cervical and intracranial arterial anomalies in 70 patients with PHACE syndrome.

C P CP Hess, H J HJ Fullerton, D W DW Metry, B A BA Drolet, D H DH Siegel, K I KI Auguste, N N Gupta, A N AN Haggstrom, C F CF Dowd, I J IJ Frieden, and A J AJ Barkovich

AJNR Am J Neuroradiol 31(10):1980-6 (2010) PMID 20705698

Cerebral and cervical arterial abnormalities are the most common non-cutaneous anomaly in PHACE syndrome, but the location and type of arterial lesions that occur have not been systematically assessed in a large cohort. Our aim was to characterize the phenotypic spectrum of arteriopathy, assess the frequency with which different arteries are involved, and evaluate spatial relationships between arteriopathy, brain structural lesions, and hemangiomas in PHACE syndrome.

DOI: 10.3174/ajnr.A2206
Version: za2963e q8zae q8zb2 q8zcc q8zd6 q8zee q8zf4 q8zg1

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