Latest papers

Cystic fibrosis and CRMS screening: what the primary care pediatrician should know.

Origins of outcome disparities in pediatric respiratory disease.

The lipid A of Burkholderia multivorans C1576 smooth-type lipopolysaccharide and its pro-inflammatory activity in a cystic fibrosis airways model.

This issue: pulmonology.

Cystic fibrosis camps.

Acute regulation of the epithelial sodium channel in airway epithelia by proteases and trafficking.

Infection with transmissible strains of Pseudomonas aeruginosa and clinical outcomes in adults with cystic fibrosis.

The cystic fibrosis-causing mutation deltaF508 affects multiple steps in cystic fibrosis transmembrane conductance regulator biogenesis.

Emerging issues in cystic fibrosis newborn screening.

Cystic fibrosis: year in review.

Aminoglycoside use in cystic fibrosis: therapeutic strategies and toxicity.

Allergic bronchopulmonary aspergillosis and Aspergillus infection in cystic fibrosis.

Impact of cystic fibrosis on bone health.

Cystic fibrosis transmembrane conductance regulator protein repair as a therapeutic strategy in cystic fibrosis.

Proceedings of a working group on 'Fungal Respiratory Infections in Cystic Fibrosis', June 7-8, 2009, Angers, France.

The opening interrupter technique for respiratory resistance measurements in children.

The use of sweat chloride test for screening cystic fibrosis among malnourished children suffering from frequent respiratory infections.

AAV's anatomy: roadmap for optimizing vectors for translational success.

Chronic hepatitis C treatment in a cystic fibrosis patient in the pulmonary pre-transplant stage.

Reducing the burden of inherited disease: the Human Variome Project.