Latest papers

Preclinical evidence that sildenafil and vardenafil activate chloride transport in cystic fibrosis.

Stimulation of salivary secretion in vivo by CFTR potentiators in Cftr+/+ and Cftr-/- mice.

Persistent osteopenia in adult cystic fibrosis transmembrane conductance regulator-deficient mice.

Very mild disease phenotype of congenic CftrTgH(neoim)Hgu cystic fibrosis mice.

Rectal potential difference and the functional expression of CFTR in the gastrointestinal epithelia in cystic fibrosis mouse models.

Partial correction of the CFTR-dependent ABPA mouse model with recombinant adeno-associated virus gene transfer of truncated CFTR gene.

Fenretinide corrects newly found ceramide deficiency in cystic fibrosis.

Impact of nutrition on phenotype in CFTR-deficient mice.

Effects of laxative and N-acetylcysteine on mucus accumulation, bacterial load, transit, and inflammation in the cystic fibrosis mouse small intestine.

Olfactory epithelia exhibit progressive functional and morphological defects in CF mice.

The inexhaustible mouse nose. Focus on "olfactory epithelia exhibit progressive functional and morphological defects in CF mice".

The role of cystic fibrosis transmembrane conductance regulator chloride channel in beta-receptor-mediated regulation of alveolar fluid clearance.

Intestinal phenotype of variable-weight cystic fibrosis knockout mice.

A role for CFTR in the elevation of glutathione levels in the lung by oral glutathione administration.

Long-term docosahexaenoic acid therapy in a congenic murine model of cystic fibrosis.

Characterisation of chloride currents across the proximal colon in CftrTgH(neoim)1Hgu congenic mice.

Elevated hepatic SULT1E1 activity in mouse models of cystic fibrosis alters the regulation of estrogen responsive proteins.

Basal cells of the human adult airway surface epithelium retain transit-amplifying cell properties.

Absence of CFTR is associated with pleiotropic effects on mucins in mouse gallbladder epithelial cells.

Mitochondrial oxidative stress in the lungs of cystic fibrosis transmembrane conductance regulator protein mutant mice.